When the balance is broken: X-linked gene dosage from two X chromosomes and female-biased autoimmunity

Abstract

Women and men exhibit differences in innate and adaptive immunity, and women are more susceptible to numerous autoimmune disorders. Two or more X chromosomes increases the risk for some autoimmune diseases, and increased expression of some X-linked immune genes is frequently observed in female lymphocytes from autoimmune patients. Evidence from mouse models of autoimmunity also supports the idea that increased expression of X-linked genes is a feature of female-biased autoimmunity. Recent studies have begun to elucidate the correlation between abnormal X-chromosome inactivation (XCI), an essential mechanism female somatic cells use to equalize X-linked gene dosage between the sexes, and autoimmunity in lymphocytes. In this review, we highlight research describing overexpression of X-linked immunity-related genes and female-biased autoimmunity in both humans and mouse models, and make connections with our recent work elucidating lymphocyte-specific mechanisms of XCI maintenance that become altered in lupus patients.

Document Details

Document Type
Pub Defense Publication
Publication Date
May 24, 2019
Source ID
10.1002/jlb.6ri0319-094r

Entities

People

  • Camille M. Syrett
  • Montserrat C Anguera

Organizations

  • National Science Foundation
  • United States Department of Defense
  • University of Pennsylvania

Tags

Fields of Study

  • Biology
  • Medicine

Readers

  • Immunology
  • Molecular and genetic basis of cancer.