Leg muscle function and fatigue during walking in spinal muscular atrophy type 3

Abstract

Introduction: Spinal muscular atrophy (SMA) causes muscle weakness and fatigue. Better understanding of the relationship between weakness and fatigue may help identify potential targets for rehabilitation. Methods: Gait and surface electromyography (EMG) from 4 muscle groups were measured during the Six‐Minute Walk Test (6MWT) in 10 ambulatory participants, aged 9–49 years. Average root mean square amplitude (RMS) of muscle activity was calculated. Strength was assessed using manual and quantitative methods. Results: RMS, stride length, and velocity decreased during the 6MWT. Knee flexor and hip abductor strength was associated with fatigue‐related changes; overall strength correlated with disease duration; and leg strength was associated with 6MWT distance. Conclusions: Clinical measures are valid in assessing fatigue and function in SMA, and these assessments can be enhanced by use of gait analysis and EMG. Disease duration and strength measures may represent further stratification refinements when enrolling patients in clinical trials. Muscle Nerve 50: 34–39, 2014

Document Details

Document Type
Pub Defense Publication
Publication Date
May 05, 2014
Source ID
10.1002/mus.24081

Entities

People

  • Ashwini K. Rao
  • Carol Ewing Garber
  • Claudia A. Chiriboga
  • Darryl C. De Vivo
  • Jacqueline Montes
  • Sally Dunaway

Organizations

  • Columbia University
  • Spinal Muscular Atrophy Foundation
  • United States Department of Defense

Tags

Fields of Study

  • Medicine

Readers

  • Computational Modeling and Simulation
  • Exercise and Sports Science.
  • Neuroscience