Enhanced Degradation of Mutant C9ORF72-Derived Toxic Dipeptide Repeat Proteins by 20S Proteasome Activation Results in Restoration of Proteostasis and Neuroprotection

Document Details

Document Type
Pub Defense Publication
Publication Date
Apr 04, 2023
Source ID
10.1021/acschemneuro.2c00732

Entities

People

  • Allison S. Vanecek
  • Jelena Mojsilovic-petrovic
  • Jetze J Tepe
  • Robert G. Kalb

Organizations

  • Les Turner ALS Foundation
  • Michigan State University
  • National Institute on Aging
  • Northwestern University
  • United States Army
  • United States Public Health Service