CDK4/6 inhibitors target SMARCA4-determined cyclin D1 deficiency in hypercalcemic small cell carcinoma of the ovary

Abstract

Inactivating mutations in SMARCA4 (BRG1), a key SWI/SNF chromatin remodelling gene, underlie small cell carcinoma of the ovary, hypercalcemic type (SCCOHT). To reveal its druggable vulnerabilities, we perform kinase-focused RNAi screens and uncover that SMARCA4-deficient SCCOHT cells are highly sensitive to the inhibition of cyclin-dependent kinase 4/6 (CDK4/6). SMARCA4 loss causes profound downregulation of cyclin D1, which limits CDK4/6 kinase activity in SCCOHT cells and leads to in vitro and in vivo susceptibility to CDK4/6 inhibitors. SCCOHT patient tumors are deficient in cyclin D1 yet retain the retinoblastoma-proficient/p16INK4a-deficient profile associated with positive responses to CDK4/6 inhibitors. Thus, our findings indicate that CDK4/6 inhibitors, approved for a breast cancer subtype addicted to CDK4/6 activation, could be repurposed to treat SCCOHT. Moreover, our study suggests a novel paradigm whereby critically low oncogene levels, caused by loss of a driver tumor suppressor, may also be exploited therapeutically.

Document Details

Document Type
Pub Defense Publication
Publication Date
Feb 04, 2019
Source ID
10.1038/s41467-018-06958-9

Entities

People

  • Alexander R. Judkins
  • Alexandra Leary
  • Andreas I. Papadakis
  • Atefeh Abedini
  • Aurelie Auguste
  • Barbara Vanderhyden
  • Blaise A. Clarke
  • Brian Meehan
  • Daniel Martinez
  • Douglas A Levine
  • Elizabeth A MacDonald
  • Geneviève Morin
  • Hongbo Chen
  • Iris De Rink
  • Janusz Rak
  • Jay Patibandla
  • Jerry Pelletier
  • Josée Dostie
  • Leora Witkowski
  • Marie-christine Guiot
  • Michael Witcher
  • Michelle Firlit
  • Morag Park
  • Nicholas Bertos
  • Petar Jelinic
  • Radia M. Johnson
  • Ralf Hass
  • Regina Cencic
  • Ron M. Kerkhoven
  • Sidong Huang
  • Sriram Venneti
  • Tim Kong
  • Walter H. Gotlieb
  • William David Foulkes
  • Xue Qing D. Wang
  • Yibo Xue

Organizations

  • Canadian HIV Trials Network, Canadian Institutes of Health Research
  • Canadian Institutes of Health Research
  • Congressionally Directed Medical Research Programs

Tags

Fields of Study

  • Medicine

Readers

  • Information Retrieval
  • Molecular Biology and Genetics
  • Oncology