Cell type-specific lipid storage changes in Parkinson’s disease patient brains are recapitulated by experimental glycolipid disturbance

Abstract

Recently, the field of Parkinson’s disease biology has shifted attention away from pure proteinotoxic hypotheses to emphasize primary cellular insults, including glycolipid disturbances. In this work, dopaminergic neurons in the Parkinson’s disease-vulnerable region of substantia nigra were found to accumulate neutral lipids, whereas in the same tissues, astrocytes have reduced lipid content, and resident microglia (a form of brain macrophage) show overall accumulation of lipids associated with inflammation. These changes were reproduced experimentally by blocking a specific lysosomal hydrolase in mice, generating a glycolipid accumulation in the animals. Based on these findings, it is reasonable to propose that restoring lipid homeostasis between neurons, astrocytes, and microglia could potentially influence PD pathogenesis and disease progression.

Document Details

Document Type
Pub Defense Publication
Publication Date
Oct 15, 2020
Source ID
10.1073/pnas.2003021117

Entities

People

  • Jonathan R Honey
  • Oeystein Roed Brekk
  • Ole Isacson
  • Penelope J. Hallett
  • Seungil Lee

Organizations

  • Harvard Medical School
  • National Institute of Neurological Disorders and Stroke
  • National Institute on Aging
  • United States Department of Defense

Tags

Fields of Study

  • Biology

Readers

  • Immunology and Pathology
  • Microbial Pathology
  • Neurodegenerative Parkinson's Disease and Rickettsial Disease handbook, including the data level of dopamine, BC, neurons, and PD.