Understanding the Delay in Onset of Pagets Disease of Bone

Abstract

One of the key questions in Pagets disease of bone (PDB) is the nature of the trigger for initiation of the disease. Inheritance of a predisposing mutation in the Sequestosome 1(SQSTM1) gene and childhood infection with Measles virus are critical, but how this leads to initiation of the disease only after a significant period of time has passed, is unclear. Understanding the genetics underlying this disease process and how the predisposing mutation interacts with the measles virus genome is the goal of this proposal. We have developed a model to compare the gene sets from significantly regulated genes affected by the measles virus genome expression in the context of the SQSTM1 mutation in human osteoblasts and carried out RNA-seq analysis on this model.

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Document Details

Document Type
Technical Report
Publication Date
Sep 01, 2015
Accession Number
AD1008512

Entities

People

  • Marc F. Hansen

Organizations

  • University of Connecticut

Tags

DTIC Thesaurus Topics

  • Amino Acids
  • Biology
  • Cell Line
  • Cells
  • Computational Biology
  • Culture Techniques
  • Gene Expression
  • Genetic Phenomena
  • Genetic Structures
  • Genetics
  • Infection
  • Medical Personnel
  • Mutations
  • Osteoblasts
  • Proteins
  • Systems Biology
  • Wound Infections

Fields of Study

  • Biology

Readers

  • Molecular Genetics
  • Neurological Diseases/Conditions/Disorders
  • Oncology

Technology Areas

  • Biotechnology