Developing Gene Silencing for the Study and Treatment of Dystonia

Abstract

Dystonia is a disabling and incurable neurological disorder characterized by twisting movements that cause significant disability. Some forms of dystonia are caused by genetic mutations and, therefore, passed on from generation to generation. The most common form of early onset genetic dystonia is a disease known as DYT1, in which children around age ten develop dystonia, usually in a leg or arm, and over 2 or 3 years spreads to affect all body parts causing substantial disability. There is no cure for DYT1. Therefore, the development of new treatments for DYT1 is a priority in dystonia research.

Open PDF

Document Details

Document Type
Technical Report
Publication Date
Oct 01, 2016
Accession Number
AD1017037

Entities

People

  • Pedro Gonzalez-alegre

Organizations

  • Children's Hospital of Philadelphia

Tags

DTIC Thesaurus Topics

  • Brain
  • Cells
  • Cerebellum
  • Demographic Cohorts
  • Diseases And Disorders
  • Gene Therapy
  • Genes
  • Genetic Phenomena
  • Genetically Modified Organisms
  • Genetics
  • Health Services
  • Medical Personnel
  • Movement Disorders
  • Neurodegeneration
  • Therapy
  • Toxicity

Readers

  • Manufacturing Engineering.
  • Neuroscience
  • Women's Health and Cancer Risk Research: African American Women and Pregnancy Outcomes.

Technology Areas

  • Biotechnology