Multiple co-morbid conditions in patient with Mast Cell Activation Syndrome
Abstract
Mast cell activation disorders (MCAD) have been associatedwith Connective Tissue Disorders (CTD) and orthostatic intolerance and/or postural orthostatic tachycardia syndrome (POTS) in limited reports. A single report has also identified kindreds of patients with an autosomal dominant pattern of increased serum tryptase and variably associated CTD, neuropsychiatric findings, atopy, and gastrointestinal disorders. This abstract describes an unusual case of MCAD; Ehlers-Danlos Hypermobility Syndrome (EDHS); orthostatic intolerance; anxiety/ADHD; intermittent diarrhea; and a carcinoid tumor. This cluster of co-morbid conditions with MCAD has not been described to occur in a single patient.
Document Details
- Document Type
- Technical Report
- Publication Date
- Oct 26, 2017
- Accession Number
- AD1040696
Entities
People
- Sofia Szari
Organizations
- 59th Medical Wing