Macrophage Responses to Epithelial Dysfunction Promote Lung Fibrosis in Aging

Abstract

Aim 1 and 2: Using mouse models of lung injury, fibrosis and epithelial dysfunction, we have demonstrated that microenvironment is a key factor driving phenotype of profibrotic alveolar macrophages. We have shown that epithelial dysfunction promotes recruitment of monocyte-derived alveolar macrophages and leads to exaggerated pulmonary fibrosis. Aim 3. Pulmonary fibrosis is a heterogeneous syndrome in which fibrotic scar replaces normal lung tissue. We performed massively parallel single-cell RNA-Seq on lung tissue from eight lung transplant donors and eight patients with pulmonary fibrosis. Combined with in situ RNA hybridization, with amplification, these data provide a molecular atlas of disease pathobiology. We identified a distinct, novel population of profibrotic alveolar macrophages exclusively in patients with fibrosis. Within epithelial cells, the expression of genes involved in Wnt secretion and response was restricted to non-overlapping cells. We identified rare cell populations including airway stem cells and senescent cells emerging during pulmonary fibrosis. Analysis of a cryobiopsy specimen from a patient with early disease supports the clinical application of single-cell RNA-Seq to develop personalized approaches to therapy.

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Document Details

Document Type
Technical Report
Publication Date
Oct 01, 2018
Accession Number
AD1064064

Entities

People

  • Alexander V. Misharin

Organizations

  • Northwestern University

Tags

DTIC Thesaurus Topics

  • Bone Marrow
  • Cells
  • Computational Biology
  • Diseases And Disorders
  • Dysfunction
  • Epithelial Cells
  • Genes
  • Lung Diseases
  • Macrophages
  • Medical Personnel
  • Monocytes
  • Systems Biology
  • Tissue Donors
  • Wounds And Injuries

Fields of Study

  • Biology
  • Medicine

Readers

  • Immunology and Pathology

Technology Areas

  • Biotechnology