Regulation of Cardiogenesis by GATA Transcription Factors

Abstract

In the first year of this project, we were able to evaluate loss of function mutations for gata4, gata5, and gata6, in both zebrafish and human ESC models. We were surprised to find that gata4 null mutations were tolerated in zebrafish, while the gata5 and gata6 mutations phenocopied previous analyses including a small truncated heart tube for gata6 mutants. We used western blotting to demonstrate that the gata4 mutation is null. Most strikingly, aged mutant adults showed a severe cardiomyopathy. The heart is enlarged at least two-fold in size. We are currently characterizing hearts by histology to determine if the gata4 mutants may be a model for human dilated cardiomyopathy or some other specific disorder. This is an exciting result that supports our underlying hypothesis that the mutants can be used to model human congenital cardiac disease. In addition, we found a striking defect in cardiogenesis in the human GATA6 null mutant ESCs. We correlated this with a sharp increase in expression of RALDH2, suggesting that GATA6 normally restricts retinoid signaling important forcardiac differentiation.

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Document Details

Document Type
Technical Report
Publication Date
Jan 01, 2021
Accession Number
AD1135271

Entities

People

  • Todd Evans

Organizations

  • Cornell University

Tags

DTIC Thesaurus Topics

  • Biological Sciences
  • Biomedical Research
  • Cardiomyopathies
  • Cells
  • Department Of Defense
  • Diseases And Disorders
  • Embryos
  • Fish
  • Genes
  • Genetics
  • Heart
  • Heart Diseases
  • Instructors
  • Medical Personnel
  • Stem Cells
  • Transcription Factors
  • Universities

Fields of Study

  • Biology

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