Anesthetic Management of Catecholaminergic Polymorphic Ventricular Tachycardia in Pregnancy
Abstract
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a rare familial or de novo mutation in either the cardiac RyR2 Ryanodine gene (CPVT1) or CASQ2 calsequestrin gene (CPVT2). Both of these mutations alter normal cardiac myocyte calcium regulation, enhancing the propensity of sarcoplasmic reticulum calcium to be released. These spontaneous calcium discharges cause unpredictable malignant arrhythmias presenting as syncope or sudden cardiac death.
Document Details
- Document Type
- Technical Report
- Publication Date
- Nov 01, 2021
- Accession Number
- AD1151857
Entities
People
- Christopher J. Nagy
- Courtney R. Hood
Organizations
- 59th Medical Wing