Surgical Aortic Valve Replacement for the Patient with Stiff Person Syndrome

Abstract

Stiff Person Syndrome (SPS) is a rare neuromuscular condition characterized by axial and proximal muscle stiffness and rigidity, with superimposed spasms, occurring in approximately 1-2 : 1 million patients. It is associated with certain HLA genes but has no known genetic inheritance pattern.1It can exist concurrently with other autoimmune conditions such as vitiligo, diabetes mellitus, thyroiditis, and pernicious anemia. Cancer may predispose the development of SPS as well.3

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Document Details

Document Type
Technical Report
Publication Date
Nov 01, 2021
Accession Number
AD1151865

Entities

People

  • Nicholas K Lahvic
  • Timothy Mooney

Organizations

  • 59th Medical Wing

Tags

DTIC Thesaurus Topics

  • Airway Management
  • Anticonvulsants
  • Autoimmune Diseases
  • Blood
  • Cardiovascular Physiological Phenomena
  • Cardiovascular Surgery
  • Cardiovascular System
  • Catheters
  • Death
  • Diseases And Disorders
  • Drug Abuse
  • Heart Diseases
  • Heart Valve Diseases
  • Heart Valves
  • Hematologic Diseases
  • Infection
  • Magnesium Compounds
  • Medical Personnel
  • Myocardial Ischemia
  • Respiration Disorders
  • Skeletal Muscle
  • Surgery
  • Therapy

Fields of Study

  • Medicine

Readers

  • Immunology
  • Molecular and genetic basis of cancer.
  • Neurotrauma and Rehabilitation Medicine.

Technology Areas

  • Biotechnology