Management of Mitochondrial Disorders Through Increased Intestinal Fermentation and Reduced Metabolic Burden

Abstract

This proposal explores the role of the microbiome and management of mitochondrial disease. Aim 1 proposes to obtain high quality sequencing data from a mouse model of mitochondria disease at different stages of disease, as well as from animals treated with acarbose, a drug known to alter the composition of the intestinal microbiome. Aim2 explores therapeutic approaches based on alterations of the intestinal microbiomes composition or activity, either through microbiome transplantation or treatment with fermentable carbon sources or fermentation products.We have gathered most of the samples required for Aim 1 and attempted microbiome transfers in breeder animals as suggested in the original proposal. We have discovered that germ-free animals are longer lived than animals in specific pathogen free facilities. However, microbiome transfers were inconclusive. We are attempting a different strategy for the transfer experiments.

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Document Details

Document Type
Technical Report
Publication Date
Jan 01, 2024
Accession Number
AD1228215

Entities

People

  • Alessandro Bitto

Organizations

  • University of Washington

Tags

Fields of Study

  • Biology

Readers

  • Immunology and Pathology
  • Microbial Pathology
  • Systems Analysis and Design

Technology Areas

  • Biotechnology