Alpha Synuclein in a Model of Multiple System Atrophy
Abstract
Multiple system atrophy (MSA) is a progressive neurological disorder characterized by parkinsonism, cerebellar dysfiinction and autonomic impairment. The cardinal pathological feature of MSA is the glial cytoplasmic inclusion (GCI) in oligodendrocytes, and a major component of GCIs is oc-synuclein. We identified a rat oligodendrocytic precursor cell line (CG-4) that produces a-synuclein and characterized oc-synuclein in the cells and production of a-synuclein after differentiation to mature oligodendrocytes and astrocytes. Studies to date suggest that oxidative stress can cause aggregation of a-synuclein. We have further developed CG-4 cells that can overexpress human a-synuclein constitutively or under the control of a tetracycline inducible promoter.
Document Details
- Document Type
- Technical Report
- Publication Date
- Sep 01, 2002
- Accession Number
- ADA409812