Role of RASGRF1 in Neurofibromatosis - Validating a Potential Therapeutic Target

Abstract

It was hypothesized that the gene encoding the RASGRF1 protein, a GTP exchange factor (GEF), controls the severity of neurofibromatosis. Over-expression of the Rasgrf1 gene was predicted to exacerbate neurofibromatosis while Rasgrf1 silencing will attenuate it. Two novel strains of mice ideally suited to test this hypothesis that were developed in my lab were used to evaluate the role or RASGRF1 on the manisfestations of neurofibromatosis type 1. One strain of mice over-express Rasgrf1, the other has diminished expression. These were crossed with a mouse model for NF1 and the effects of the altered level of RASGRF1 protein on tumorigenesis were monitored. The results of these studies support the hypothesis that attenuating the GEF activity of RASGRF1 protein also attenuates tumorigenic pathways controlled by NF1. Also, in characterizing the strains of mice we developed for this study, we obtained new insights into the regulation and functions of the Rasgrf1 gene.

Open PDF

Document Details

Document Type
Technical Report
Publication Date
Apr 01, 2006
Accession Number
ADA460497

Entities

People

  • Paul D. Soloway

Organizations

  • Cornell University

Tags

DTIC Thesaurus Topics

  • Cells
  • Chemistry
  • Erythrocytes
  • Genetics
  • Health Services
  • Intellectual Property
  • Law
  • Materials
  • Neoplasms
  • Nervous System
  • Neurofibromatosis
  • Neuromuscular Diseases
  • New York
  • Nucleotides
  • Nutritional Sciences
  • Regulations
  • Stem Cells

Fields of Study

  • Biology

Readers

  • Molecular Biology and Genetics
  • Neurological Diseases/Conditions/Disorders