New Structural Approaches to Understanding the Disease Related Forms of the Prion Protein

Abstract

The mouse pron protein peptide (residues 89-143 with the substitution of Leu for Pro atresidue 101) induces prion disease in sensitized mice. Samples of this peptide, isotope labeled with 15N, have been prepared by expression of a fusion in E.coli, cleaved to yield anunmodified peptide, and then fibrillized. Hydrogen exchange was allowed to occur in the fibrils for periods from 1 hour to 6 weeks. The extent of exchange was monitored using peak intensities in 15N-1H HSQC nuclear magnetic resonance spectra in DMSO/D2O/TFA solutions that had previously been assigned. The exchange data show a high fraction of amides are protected,with a core set (residues 104-109 and 117-135) exchanging very slowly (<10% exchange in 6 weeks). Some biphasic exchange was observed for residues between 110 and 116 suggesting aconformationally heterogeneous region, possibly relating to strain behavior. Samples of unlabeled, uniformly 13C/15N labeled and selectively 13C labeled peptide were prepared for solid state NMR experiments.

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Document Details

Document Type
Technical Report
Publication Date
Jul 01, 2006
Accession Number
ADA468058

Entities

People

  • David E Wemmer

Organizations

  • University of California Regents

Tags

Communities of Interest

  • Biomedical

DTIC Thesaurus Topics

  • Amino Acids
  • Chemical Shifts
  • Chemical Synthesis
  • Chemistry
  • Crystal Structure
  • Crystallography
  • Diffraction
  • Magnetic Resonance
  • Materials
  • Materials Science
  • Molecular Dynamics
  • Neurodegeneration
  • Nuclear Magnetic Resonance
  • Peptides
  • Resonance
  • Spectra
  • Two Dimensional

Readers

  • Criminal Law
  • Immunology
  • Molecular and Cellular Biochemistry