Novel Molecular Interactions and Biological Functions of the Neurofibromatosis 2 Tumor Suppressor Protein, Merlin

Abstract

The project studies molecular functions of neurofibromatosis 2 tumor suppressor protein merlin and the ERM protein ezrin. Phosphorylation is an important mechanism in theregulation of both proteins. We have studied the interplay between protein kinase A (PKA) andmerlin. We identified an N-terminal phosphorylation site at merlin S10. Phosphorylation of S10 does not affect phosphorylation of S518 or ezrin binding. It affects, however, actin dynamics and cell morphology and migration in Nf2 -/- mouse embryonic fibroblasts (MEF) and Schwann cells. This suggests a role for merlinin mediating PKA induced changes of the actin cytoskeleton. We also show a link between PKA and calpain in the regulation of merlin cleavage and subcellular localization. We previously showed that oncogenic tyronsine kinase Src phosphorylates ezrin at Y477. Using reconstituted MEF cells from ezrin -/- mice we studied the biological importance of Y477 phosphorylation. Our results show that ezrin is a key regulator of Src induced malignant behavior in three dimentional culture conditions.

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Document Details

Document Type
Technical Report
Publication Date
Aug 01, 2008
Accession Number
ADA483204

Entities

People

  • Olli Carpen

Organizations

  • University of Helsinki

Tags

DTIC Thesaurus Topics

  • Breast Cancer
  • Cell Line
  • Cell Membrane
  • Cell Movement
  • Cell Physiological Processes
  • Cells
  • Cellular Structures
  • Chemistry
  • Confocal Microscopy
  • Cytoskeleton
  • Epithelial Cells
  • Genetics
  • Health Services
  • Medical Personnel
  • Proteins
  • Three Dimensional

Fields of Study

  • Biology

Readers

  • Cellular and Molecular Pathways of Apoptosis.
  • Neurological Diseases/Conditions/Disorders