Severe Tissue Trauma Triggers the Autoimmune State Systemic Lupus Erythematosus in the MRL/++ Lupus-Prone Mouse

Abstract

Tissue damage associated with a severe injury can result in profound inflammatory responses that may trigger autoimmune development in lupus-prone individuals. In this study, we investigated the role of a large full-thickness cutaneous bum injury on the early onset of autoimmune disease in lupus-prone MRL/++ mice. MRL/++ mice (chronic model) exhibit autoimmune symptoms at >70 weeks of age, whereas MRL/-Fas1pr mice (acute model) develop autoimmune disease in 1722 weeks due to a lymphoproliferative mutation. Autoimmune disease developed in MRL/++ mice (4-15 weeks post injury) is manifested by skin lesions, vasculitis, epidermal ulcers, cellular infiltration, splenomegaly, lymphadenopathy, hypergammaglobulinemia, elevated autoantibodies and renal pathologies including proteinuria, glomerulonephritis and immune complex deposition; complications that contribute to reduced survival. Transcription studies of wound margin tissue show a correlation between the pathogenic effects of dysregulated IL-1beta p, IL-6, TNF-alpha and PGE2 synthesis during early wound healing and early onset of autoimmune disease. Interestingly, MRL/++ mice with healed wounds (30-40 days post burn) strongly rejected skin isografts. Conversely, skin isografts transplanted onto naive age-matched MRL/++ littermates achieved long-term survival. Collectively, these findings suggest that traumatic injury exacerbates inflammatory skin disease and severe multi-organ pathogenesis in lupus-prone mice.

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Document Details

Document Type
Technical Report
Publication Date
Jan 01, 2009
Accession Number
ADA506715

Entities

People

  • K. A. Szabo
  • K. Anam
  • M. Amare
  • S. Naik
  • Thomas A. Davis

Organizations

  • Naval Medical Research Center

Tags

DTIC Thesaurus Topics

  • Autoimmune Diseases
  • Autoimmunity
  • Blood
  • Cells
  • Chemistry
  • Connective Tissue Diseases
  • Dermatologic Agents
  • Diseases And Disorders
  • Gene Expression
  • Genetics
  • Kidney Diseases
  • Lupus
  • Lymphatic System
  • Lymphocytes
  • Medical Personnel
  • Proteins

Fields of Study

  • Biology
  • Medicine

Readers

  • Immunology and Pathology
  • Molecular and Cellular Biology
  • Neurological Diseases/Conditions/Disorders

Technology Areas

  • Biotechnology
  • Biotechnology - Cancer Biotech