Novel Molecular Interactions and Biological Functions of the Neurofibromatosis 2 Tumor Suppressor Protein, Merlin

Abstract

The project has studied the functions of the neurofibromatosis 2 tumor suppressor protein merlin and the related ERM protein ezrin. We identified novel binding partners and functions for both proteins. Merlin was shown to regulate both the microtubule and actin cytoskeleton. Two important kinases, protein kinase A (PKA) and AKT, were shown to phosphorylate merlin at S10. This phosphorylation affects actin dynamics, cell morphology and migration of mouse embryonic fibroblasts (MEF) and Schwann cells. Thus, merlin may serve as a regulator of PKA and AKT induced changes in actin cytoskeleton. We identified a link between merlin and cell cycle control by demonstrating a novel functional interaction between merlin and HEI10. In studies of the biological activities of ezrin we discovered that oncogenic tyrosine kinases Src and c-Met phosphorylate ezrin at Y477. Using reconstituted MEF cells from ezrin -/- mice we studied the biological importance of Y477 phosphorylation. Our results show that ezrin is a key regulator of Src induced malignant behavior in three dimensional culture conditions.

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Document Details

Document Type
Technical Report
Publication Date
Aug 01, 2008
Accession Number
ADA510232

Entities

People

  • Olli Carpen

Organizations

  • University of Helsinki

Tags

DTIC Thesaurus Topics

  • Breast Cancer
  • Cell Movement
  • Cell Physiological Processes
  • Cells
  • Chemistry
  • Cytoskeleton
  • Genetics
  • Health Services
  • Medical Personnel
  • Proteins
  • Three Dimensional

Fields of Study

  • Biology

Readers

  • Breast cancer cell signaling and growth regulation.
  • Molecular Biology and Genetics
  • Neurological Diseases/Conditions/Disorders