Molecular Regulation of Endothelial Cells by NF-1

Abstract

We have a manuscript accepted that demonstrates the role of NF1in endothelial cell function. We have validated siRNA, antibodies, and inducible shRNA specific for individual Ras isoforms and used them to measure the regulation of Ras isoforms following loss of NF1 and their contributions to endothelial regulation, as well as the sufficiency of these isoforms to mimic the loss of NF1. As mTOR is critical to NF1 regulation, we investigated the role of this axis in endothelial cells. Lastly our attempts to create an in-vivo model of NF1 disease in the vasculature continue. We have succeeded in obtaining highly penetrant endothelial specific recombination. We have also bred this mouse onto the NF1 flox/flox background and evaluation of this phenotype is ongoing. We have in place a number of staining protocols and isolation procedures for biochemical analysis which should accelerate the determination of the effects in these mice. While this aspect of our proposed work has moved slower than anticipated, we are confident we now have the basis for an endothelial cell specific model of NF1.

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Document Details

Document Type
Technical Report
Publication Date
Jul 01, 2012
Accession Number
ADA567663

Entities

People

  • Kevin Pumiglia

Organizations

  • Albany Medical College

Tags

DTIC Thesaurus Topics

  • Arteries
  • Blood
  • Cardiovascular Diseases
  • Cardiovascular System
  • Cell Physiological Processes
  • Cells
  • Cerebrovascular Disorders
  • Congenital Abnormalities
  • Culture Techniques
  • Diseases And Disorders
  • Endothelial Cells
  • Growth Factors
  • Neuromuscular Diseases
  • Proteins
  • Vascular Diseases
  • Vascular Endothelium
  • Vascular Malformations

Fields of Study

  • Biology
  • Medicine

Readers

  • Oncology (Cancer Research).
  • Systems Analysis and Design