Apo-Ferritin as a Therapeutic Treatment for Amyotrophic Lateral Sclerosis

Abstract

Iron accumulation and deposition have been reported in patients with amyotrophic lateral sclerosis (ALS). Previous work in mutant SOD1 mice mouse models of ALS have indicated that iron chelation with a chemical agent extends lifespan. Therefore, we propose the use of apo-ferritin, the iron-storage protein ferritin that is iron poor, as a natural ionophore to sequester excess iron and redistribute it. The overall hypothesis is that infusion of apo-ferritin protein into the brain will provide neuroprotection by limiting the availability of excess iron to catalyze free-radical production. The most significant finding from the first year of funding is that infusion of artificial cerebrospinal fluid containing nutrients, including H-ferritin, increases lifespan and delays onset of disease in SOD1G93A mice. Furthermore, the number of motor neurons in the lumbar spinal cord at endpoint is greater in mice that received infusion versus those that did not. The potential clinical significance of this work is that increasing turn-over of cerebrospinal fluid should be further explored as a therapeutic option in ALS.

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Document Details

Document Type
Technical Report
Publication Date
Sep 01, 2012
Accession Number
ADA567828

Entities

People

  • James R. Connor

Organizations

  • Pennsylvania State University

Tags

DTIC Thesaurus Topics

  • Anesthesia
  • Availability
  • Brain
  • Central Nervous System
  • Diseases And Disorders
  • Free Radicals
  • Infusions
  • Motor Neurons
  • Nervous System
  • Neurodegenerative Diseases
  • Neurons
  • Pain
  • Production
  • Sclerosis
  • Spinal Cord
  • Surgery
  • Therapy

Fields of Study

  • Biology

Readers

  • Medical Imaging.
  • Neuroscience