Neuroprotective Small Molecules for the Treatment of Amyotrophic Lateral Sclerosis

Abstract

Amyotrophic Lateral Sclerosis (ALS) is a progressive neurodegenerative disease for which there is no cure. Because of the lack of understanding of the cause of ALS, treatment is limited to mechanical intervention and riluzole, both of which extend existence rather than extend life. Thus, there is an urgent need to find drugs that are of some benefit to ALS. To this end, we are developing a cell-based co-culture high throughput screening system which is composed of mutant SOD1 astrocyte-conditioned medium (ACM), ES-MNs and a high-throughput screening robot, that we believe, will give faster screening of chemicals and drugs to treat ALS. We have, thus far, validated our co-culture system, validated that our high throughput screening technique works and miniaturized our system to a 96 well plate. Z?-factor (between 0.5-1.0) is a measure of how good an assay is. At present, our Z?-factor is 0.3, and we are working on improving this value. Nonetheless, we have identified 108 compounds, from our first screen from chemical libraries, that have a wide range of actions. Of these 108 compounds, five have reached the second screen stage and two of the five hold good possibilities. With our system, we noted that JNK2/3 inhibitors are protective for primary motor neurons and ES-MNs) which was confirmed on a low throughput screen. Compared to other high throughput screening systems, our readout is simple: survival of ES-MNs in ACM treated with one of the hits from our high throughput screen coculture system seems to be successful in finding small molecules that are possibilities for the treatment of ALS.

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Document Details

Document Type
Technical Report
Publication Date
Sep 30, 2012
Accession Number
ADA567841

Entities

People

  • Serge Przedborski

Organizations

  • Columbia University

Tags

DTIC Thesaurus Topics

  • Biological Products
  • Cell Line
  • Cell Physiological Processes
  • Cells
  • Culture Media
  • Culture Techniques
  • Diseases And Disorders
  • Dynamic Range
  • Inhibition
  • Molecules
  • Motor Neurons
  • Neurodegenerative Diseases
  • Neuroglia
  • Neurons
  • Small Molecules
  • Spinal Cord
  • Stem Cells

Fields of Study

  • Medicine

Readers

  • Molecular Genetics
  • Oncology
  • Oncology and Biomarker-Based Cancer Detection.

Technology Areas

  • AI & ML
  • Autonomy