Treating Combat Hearing Loss with Atoh1 Gene Therapy

Abstract

The goal of the project is to test experimental therapies for hearing loss in transgenic mouse models. We have developed molecular methods to identify sensory hair cells in the inner ear, including two different validated genetic profiles of sensory hair cells. We have generated and derived genetically modified mice to serve as models for treating hearing loss with gene therapy. We have shown that five such models are not suitable for our studies, but we have genetically engineered two new mouse lines line and re-derived a third line from our collaborators. We have also generated data to determine the genetic differences in supporting cells of the cochlea at two different ages, and to determine the response of these cells to pharmacological inhibitors that may promote hair cell regeneration.

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Document Details

Document Type
Technical Report
Publication Date
Oct 01, 2012
Accession Number
ADA613968

Entities

People

  • Andrew K. Groves

Organizations

  • Baylor College of Medicine

Tags

DTIC Thesaurus Topics

  • Cell Physiological Processes
  • Cells
  • Diseases And Disorders
  • Ear
  • Gene Expression
  • Gene Therapy
  • Genes
  • Genetics
  • Hearing Disorders
  • Hearing Loss
  • Inhibitors
  • Medical Personnel
  • Organ Of Corti
  • Proteins
  • Rna Sequence Analysis
  • Therapy

Fields of Study

  • Biology

Readers

  • Auditory Neuroscience/Auditory Physiology.
  • Computational Modeling and Simulation
  • Molecular and genetic basis of cancer.

Technology Areas

  • Biotechnology