A Generic, High-Throughput Screening Platform for Fragile X, Rett Syndrome, and Frontotemporal Degeneration Using Human Synthetic Embryos

Abstract

Fragile X, Rett syndrome, and frontotemporal degeneration are three devastating, rare neurological disorders that lack effective treatments, with authorized drugs that do exist mainly focusing on managing symptoms. In this proposal, we propose to develop a tool that will allow the efficient discovery of new therapeutics for these three diseases. Our approach is to recreate, in the laboratory, the first steps of the development of the central nervous system from embryonic stem cells. When these stem cells are carrying genetic mutation associated with one of these diseases, we can easily observe defects in the organization of our developing tissues. These differences between “healthy” and “disease” tissues are analyzed and exploited to find drugs that can reverse these defects. We are convinced that drugs that can cure synthetic human developing tissues in the lab will then translate efficiently in the clinic for curing patients.

Document Details

Document Type
DoD Grant Award
Publication Date
Mar 10, 2021
Source ID
W81XWH2010060

Entities

People

  • Fred Etoc

Organizations

  • Rumi Scientific (United States)
  • United States Army

Tags

Fields of Study

  • Biology

Readers

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  • Immunology and Pathology
  • Traumatic Brain Injury (TBI) and Cognitive Aging in the Guam and Border Populations Affected by Alzheimer's Disease and Tau-Associated Dementias.

Technology Areas

  • Biotechnology